May
08
23:01
Diseases of internal organs

Ormond's disease - idiopathic retroperitoneal fibrosis

Ormond's disease - idiopathic retroperitoneal fibrosis

Ormond's disease (idiopathic retroperitoneal fibrosis, retroperitoneal fibrosis) - progressive compression of one (usually two) ureteral scar (fibrous) tissue.Often, there is complete closure of the lumen.
To date, significant causes of this disease so not fully understood

Possible causes of the disease Ormond
- Development on the basis of pelvic inflammatory disease
- cholangitis and cholecystitis
- Ileitis
- Pancreatitis
- Lymphangitis
- granulomatous vasculitis
- hematoma formed in the retroperitoneal space due to injury
In addition, researchers have immunoallergic hypothesis of occurrence in the tissue of the retroperitoneal fat fibrosis

Symptoms

- Paroxysmal dull pain in the lumbar region
- Abdominal pain in the testicles
- Loss of appetite and fatigue
- Increased blood pressure
- Increased ESR
As the disease progresses Ormond may cause complications in the form renal failure and nephrogenic hypertension

Diagnostics

Diagnosis is based on receivedexcretory urography results and review the image of the upper urinary tract.To aid retrograde ureteropyelography to determine the state of the upper urinary tract resorted to if there is a sharp decline in renal function.Also, to assess the anatomical - functional state of kidneys used radioisotope research methods (scintigraphy and isotopic renography) and to establish an accurate picture of hydronephrosis transformation is applied Ultrasonography

Treatment

Treatment depends on the extent andlocalization of the disease, the presence of urinary infection and the extent of violations of the passage of urine.In most cases, the patient is assigned to surgery.
in the postoperative period to suppress the development of fibrous tissue long enough to apply corticosteroids (hydrocortisone 25 mg daily for two - three months).Parallel to this, appointed by the other absorbable therapy (aloe lidasa)

forecast

In the absence of proper treatment Ormond disease prognosis is poor as due to the progression of chronic renal failure and due to rise hydronephrosis transformation possible death.After the surgery a more favorable prognosis, but may experience recurrence of the disease.

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